Neeraj Kumar Tulara
Dr LH Hiranandani Hospital,Hillside Avenue,
Hiranandani Gardens, Powai, Mumbai 400076
India
Case Report
Young Male with Secondary Acute Hemophagocytic Lymphohistiocytosis
Author(s): Neeraj Kumar TularaNeeraj Kumar Tulara
Hemophagocytic lymphohistiocytosis (HLH), also known as hemophagocytic syndrome (HPS), is a rare life threatening hematologic disorder manifested by clinical findings of extreme inflammation and unregulated immune activation. HLH can occur as a familial or sporadic disorder, and it can be triggered by a variety of events that disrupts immune haemostasis. Infection is a common trigger both in those with a genetic predisposition and in sporadic cases. Often the greatest barrier to a successful outcome is delay in diagnosis, which is difficult because of the rarity of this syndrome. Here we, present a case of a young male who presented with enteric fever and confirmed as acute hemophagocytic syndrome and deteriorated rapidly inspite of quick diagnosis and treatment.
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